RT Journal
A1 Groh WJ, Bhakta D
T1 ARrhythmia management in myotonic dystrophy type 1
JF JAMA
JO JAMA
YR 2012
FD July 25
VO 308
IS 4
SP 337
OP 338
DO 10.1001/jama.2012.6807
UL http://dx.doi.org/10.1001/jama.2012.6807
AB 
To the Editor: Dr Wahbi and colleagues1 concluded that sudden death mortality was improved in patients with myotonic dystrophy type 1 (DM1) and moderate conduction abnormalities on electrocardiogram who underwent an invasive strategy consisting of an electrophysiological study followed by prophylactic pacing if the HV interval exceeded 70 milliseconds. In our opinion, there are uncertainties in how the retrospective observational trial was conducted and reported that limit the ability to determine if their invasive strategy was associated with a survival advantage.