0
We're unable to sign you in at this time. Please try again in a few minutes.
Retry
We were able to sign you in, but your subscription(s) could not be found. Please try again in a few minutes.
Retry
There may be a problem with your account. Please contact the AMA Service Center to resolve this issue.
Contact the AMA Service Center:
Telephone: 1 (800) 262-2350 or 1 (312) 670-7827  *   Email: subscriptions@jamanetwork.com
Error Message ......
ARTICLE |

SUPRAVALVULAR AORTIC STENOSIS

JAMA. 1966;198(12):1302-1303. doi:10.1001/jama.1966.03110250116033.
Text Size: A A A
Published online

In the eight years since the first clinical diagnosis of supravalvular aortic stenosis, many questions regarding this entity have been raised and some have been answered. Myers and Willis,1 in the December issue of the Archives of Internal Medicine, present four cases with diverse clinical manifestations, in an effort to emphasize the broad clinical spectrum of this disease. The characteristic lesion occurs as part of a syndrome which includes an "elfin" facies, mental retardation, peripheral pulmonary artery stenosis, and supravalvular aortic stenosis. However, the lesion occurs in an isolated form almost twice as commonly as in the more easily recognized syndrome. Family studies suggest that the complete syndrome occurs sporadically while the isolated lesion occurs in families. The investigators point out that, though the lesion can present without a significant murmur, most cases may be suspected from examination of the patient. A high index of suspicion based upon knowledge

Topics

Sign in

Create a free personal account to sign up for alerts, share articles, and more.

Purchase Options

• Buy this article
• Subscribe to the journal

Figures

Tables

References

Letters

CME
Meets CME requirements for:
Browse CME for all U.S. States
Accreditation Information
The American Medical Association is accredited by the Accreditation Council for Continuing Medical Education to provide continuing medical education for physicians. The AMA designates this journal-based CME activity for a maximum of 1 AMA PRA Category 1 CreditTM per course. Physicians should claim only the credit commensurate with the extent of their participation in the activity. Physicians who complete the CME course and score at least 80% correct on the quiz are eligible for AMA PRA Category 1 CreditTM.
Note: You must get at least of the answers correct to pass this quiz.
You have not filled in all the answers to complete this quiz
The following questions were not answered:
Sorry, you have unsuccessfully completed this CME quiz with a score of
The following questions were not answered correctly:
Commitment to Change (optional):
Indicate what change(s) you will implement in your practice, if any, based on this CME course.
Your quiz results:
The filled radio buttons indicate your responses. The preferred responses are highlighted
For CME Course: A Proposed Model for Initial Assessment and Management of Acute Heart Failure Syndromes
Indicate what changes(s) you will implement in your practice, if any, based on this CME course.

Multimedia

Some tools below are only available to our subscribers or users with an online account.

Sign in

Create a free personal account to sign up for alerts, share articles, and more.

Purchase Options

• Buy this article
• Subscribe to the journal

Related Content

Customize your page view by dragging & repositioning the boxes below.

Jobs
brightcove.createExperiences();