Fifty-three cases of alveolar soft-part sarcoma were analyzed. Forty-six cases were followed long enough to permit collection of survival data by actuarial methods: 82.8% (±5.9%) in two years, 59% (±8.8%) in five years, and 47.1% (±9.3%) in ten years. Most tumors were noted in female patients and there seemed to be a trend toward right-sided laterality. Tumors developed in female patients at an earlier age than in male patients. The histogenesis of the tumor remains uncertain. The paucity of information and the sluggishness of tumor growth make interpretation of therapeutic effects difficult.