EPIDERMOLYSIS BULLOSA: REPORT OF A CASE WITH LESION PRESENT AT BIRTH

Epidermolysis bullosa is described by Schamberg¹ as a rare disease, characterized by the rapid formation of blebs of various sizes following the slightest physical violence. The condition usually develops in infancy or early childhood and persists until late in life. In most cases there is a distinct history of heredity, in some instances the tendency being transmitted through several generations. The blebs are formed rapidly following slight traumatism and vary in size from a pea to a silver dollar. They are irregular in shape and are often of a claret color as a result of hemorrhage into the fluid contents. The disappearance of the bleb is frequently followed by a certain degree of atrophy of the skin.

The areas attacked, Schamberg notes, are those most subject to injury, such as the hands, feet, elbows, knees and anterior surfaces of the legs. The finger-nails are often permanently lost as a